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ENGLISH SUMMARY
A previously healthy 18 year old female has repeated admissions over a
six week period to the emergency department because of seizures. She
has no previous history of epilepsy and denies any drug use. Imaging
and electroencephalogram do not indicate epilepsy. Blood sugar levels
are low on two occasions, 1.3 mmol / L and 1.7mmól / L (4.0 - 6.0 mmol
/ L). After further investigations the suspicion of an insulin-producing
tumor arises. Extensive research and imaging is conducted to look for
tumor growth without any findings. Subsequently she was sent abroad
for further evaluation with a 11C-5HTP-PET scan, selective angiography
with celiacography and an intra-arterial calcium stimulation test. She
was diagnosed with nesidioblastosis. Here we will discuss the pres-
entation and work-up of the medical case and review this rare causative
disease.
Repeated non-epileptic seizures in a previously healthy young woman – a case report
Guðrún Mist Gunnarsdóttir1, Arna Guðmundsdóttir1, Per Hellman2, Peter Stålberg2
1Landspítali University Hospital of Iceland, 2Department of Surgical Sciences, University Hospital, Uppsala University, Sweden.
Key words: repeated seizures, neuroglycopenic symptoms, noninsulinoma pancreatogenous hypoglycemia syndrome (NIPHS), endogenous hyperinsulinemic hypoglycemia, nesi-
dioblastosis.
Correspondence: Guðrún Mist Gunnarsdóttir, gudrunmi@landspitali.is
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S J Ú K R A T I L F E L L I